Meaning: Moyamoya disease is a vasculo-occlusive disease in which collateral circulation develops and it appear as "puff of smoke".
Etiology: Inherited genetic abnormalities and vascular malformations are common causetive factors.
Clinical Manifestations: most of the signs and symptoms are like signs and symptoms of stroke and epilepsy.
Diagnostic tests: Moya Moya disease can be ruled out by CT, MRI, SPECT scan, MRA.
Management: medical management includes hydration, anti-platelet and antihypertensive treatment. Surgical management includes direct and indirect revascularization.
Prognosis: prognosis is excellent in patient with surgical management before developing disabling stroke. Without treatment, Moyamoya disease can be fatal as the result of intra-cerebral haemorrhage.
Cite this article:
Rajashree Vikas Khedekar. Moyamoya Disease – A Case Review. Int. J. Nur. Edu. and Research. 2017; 5(2): 218-222. doi: 10.5958/2454-2660.2017.00047.3