Author(s):
Nimmy P S, Greeshma V R, Aiswaria S Pal
Email(s):
nimmy4msc@gmail.com , greeshmavr1@gmail.com , aiswariaspal86@gmail.com
DOI:
10.52711/2454-2660.2024.00045 
Address:
Nimmy P S1, Greeshma V R2, Aiswaria S Pal3
1Assistant Professor, Department of Child Health Nursing, Vandanam P O, Alappuzha-688005.
2Assistant Professor, Department of Child Health Nursing, Vandanam P O, Alappuzha-688005.
3Assistant Professor, Department of Child Health Nursing, Vandanam P O, Alappuzha-688005.
*Corresponding Author
Published In:
Volume - 12,
Issue - 3,
Year - 2024
ABSTRACT:
Lennox-Gastaut syndrome (LGS) is a severe form of childhood epilepsy that is defined by generalized multiple type seizures, slowness of intellectual growth, and a specific EEG disturbance. Children affected may previously had infantile spasms or underlying brain disorder, but the aetiology can be idiopathic or symptomatic. The incidence of secondary epilepsy is higher in developed countries resulting in higher the incidence of disease. Lennox-Gastaut syndrome (LGS) 18 is characterized by multiple seizure types. An axial tonic seizure is the hallmark of LGS. Later on, atypical absence, atonic and myoclonic falls and recurrent status observed. Cognitive and behavioural abnormalities are common. Gastaut syndrome is usually between 2-7 years with a peak onset between 3 to 5 years. The awake EEG record shows 2-to2.5-Hz spike-and-wave and polyspike and wave discharges, which are usually diffuse and maximal bifrontal. The prognosis is unfavourable and only a minority of patients achieves seizure control. Newer antiepileptic drugs (AEDs) like felbamate lamotrigine and topiramate have been found to be useful. Anterior corpus callostomy may reduce seizure frequency in some patients. Astatic seizures preceded by a prominent tonic component are most improved by these procedures in some cases. LGS seizures are often treatment resistant and the long-term prognosis is poor.
Cite this article:
Nimmy P S, Greeshma V R, Aiswaria S Pal. Lennox- Gastaut Syndrome (Childhood Epileptic Encephalopathy) – A Rare Case Report. International Journal of Nursing Education and Research. 2024; 12(3):212-4. doi: 10.52711/2454-2660.2024.00045
Cite(Electronic):
Nimmy P S, Greeshma V R, Aiswaria S Pal. Lennox- Gastaut Syndrome (Childhood Epileptic Encephalopathy) – A Rare Case Report. International Journal of Nursing Education and Research. 2024; 12(3):212-4. doi: 10.52711/2454-2660.2024.00045 Available on: https://ijneronline.com/AbstractView.aspx?PID=2024-12-3-13
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